Ernst O, Gottrand F, Calvo M, Michaud L, Sergent G, Mizrahi D, L'Herminé C
Department of Radiology, Radiologie Est, Centre Hospitalier Universitaire de Lille, France.
AJR Am J Roentgenol. 1998 Feb;170(2):409-12. doi: 10.2214/ajr.170.2.9456955.
This study describes the MR imaging features of congenital hepatic fibrosis in four children who were examined with MR cholangiopancreatography.
MR cholangiopancreatography effectively reveals biliary cysts, dilatation of intrahepatic bile ducts, and polycystic kidney disease, findings often associated with congenital hepatic fibrosis. This diagnosis should be suspected when these biliary and renal abnormalities are associated with hepatosplenomegaly in a patient with normal liver function.
本研究描述了4例接受磁共振胰胆管造影检查的儿童先天性肝纤维化的磁共振成像特征。
磁共振胰胆管造影能有效显示胆管囊肿、肝内胆管扩张和多囊肾病，这些表现常与先天性肝纤维化相关。当这些胆管和肾脏异常与肝功能正常患者的肝脾肿大相关时，应怀疑该诊断。
