Gasque P, Jones J, Singhrao S K, Morgan B
Department of Medical Biochemistry, University of Wales College of Medicine, Cardiff, CF4 4XX, United Kingdom.
J Exp Med. 1998 Feb 16;187(4):451-60. doi: 10.1084/jem.187.4.451.
The brain is an immunoprivileged organ isolated from the peripheral immune system. However, it has been shown that resident cells, notably astrocytes and microglia, can express numerous innate immune molecules, providing the capacity to generate a local antipathogen system. Perforin is a cytolytic protein present in the granules of cytotoxic T lymphocytes and natural killer cells. Expression in cells other than those of the hemopoetic lineage has not been described. We report here that fetal astrocytes in culture (passages 2 to 15), astrocytoma, and adult astrocytes expressed perforin. Reverse transcriptase polymerase chain reaction followed by Southern blot was carried out using multiple specific primers and all cDNAs were cloned and sequenced. Human fetal astrocyte perforin cDNA sequence was approximately 100% identical to the reported perforin cDNA cloned from T cells. Western blot analysis using monoclonal and polyclonal antiperforin peptide antibodies revealed a protein of 65 kD in both human fetal astrocyte and rat natural killer cell lysates (n = 4). Immunostaining followed by FACS(R) and confocal and electron microscopy analysis revealed that perforin was expressed by 40-50% of glial fibrillary acidic protein positive cells present in the fetal brain culture (n = 11). Perforin was not localized to granules in astrocytes but was present throughout the cytoplasm, probably in association with the endoplasmic reticulum. Perforin was not detected in normal adult brain tissue but was present in and around areas of inflammation (white and grey matter) in multiple sclerosis and neurodegenerative brains. Perforin-positive cells were identified as reactive astrocytes. These findings demonstrate that perforin expression is not unique to lymphoid cells and suggest that perforin produced by a subpopulation of astrocytes plays a role in inflammation in the brain.
大脑是一个与外周免疫系统隔离的免疫特权器官。然而,已有研究表明,驻留细胞,尤其是星形胶质细胞和小胶质细胞,能够表达多种先天免疫分子,从而具备产生局部抗病原体系统的能力。穿孔素是一种存在于细胞毒性T淋巴细胞和自然杀伤细胞颗粒中的溶细胞蛋白。尚未见其在造血谱系以外的细胞中表达的报道。我们在此报告,培养的胎儿星形胶质细胞(传代2至15代)、星形细胞瘤和成年星形胶质细胞均表达穿孔素。使用多种特异性引物进行逆转录聚合酶链反应,随后进行Southern印迹分析,并对所有cDNA进行克隆和测序。人胎儿星形胶质细胞穿孔素cDNA序列与从T细胞克隆的已报道穿孔素cDNA序列约100%相同。使用单克隆和多克隆抗穿孔素肽抗体进行的蛋白质印迹分析显示,人胎儿星形胶质细胞和大鼠自然杀伤细胞裂解物中均有一条65 kD的蛋白条带(n = 4)。免疫染色后进行荧光激活细胞分选(FACS)、共聚焦显微镜和电子显微镜分析显示,胎儿脑培养物中40%至50%的胶质纤维酸性蛋白阳性细胞表达穿孔素(n = 11)。穿孔素在星形胶质细胞中并不定位于颗粒,而是存在于整个细胞质中,可能与内质网相关。在正常成人大脑组织中未检测到穿孔素,但在多发性硬化症和神经退行性变脑的炎症区域(白质和灰质)及其周围存在穿孔素。穿孔素阳性细胞被鉴定为反应性星形胶质细胞。这些发现表明,穿孔素表达并非淋巴细胞所特有,并提示星形胶质细胞亚群产生的穿孔素在大脑炎症中起作用。