Ansari G, Reid J S
Child Dental Care Department, Glasgow Dental Hospital.
ASDC J Dent Child. 1997 Nov-Dec;64(6):429-34.
A family is reported with dentinal dysplasia type I affecting both dentitions. Presenting features included unusual mobility of the teeth, followed by early exfoliation; normal clinical shape of the crowns of the teeth, but with an amber color without any sign of attrition or abnormal loss of enamel. Radiographic findings showed pulp-chamber and root-canal obliteration, poor root formation, radiolucent linear appearance of the pulp chamber parallel to the cementoenamel junction and frequent periapical radiolucencies. Histological studies have reported large masses of calcified tubular dentin, atypical osteodentin, and also true denticle.
据报道，有一个家庭的两名成员患有I型牙本质发育不全。临床表现为牙齿异常松动，随后过早脱落；牙齿冠部临床形态正常，但呈琥珀色，无磨损迹象或釉质异常缺失。影像学检查发现髓腔和根管闭锁、牙根形成不良、髓腔平行于牙骨质釉质界处呈透射线性外观以及频繁出现根尖周透射区。组织学研究报告有大量钙化的管状牙本质、非典型骨样牙本质，还有真性牙本质小体。
