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慢性心脏传导阻滞的神经学关联

Neurological associations of chronic heart block.

作者信息

Lambert C D, Fairfax A J

出版信息

J Neurol Neurosurg Psychiatry. 1976 Jun;39(6):571-5. doi: 10.1136/jnnp.39.6.571.

DOI:10.1136/jnnp.39.6.571
PMID:950568
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC492351/
Abstract

A large group of patients with chronic heart block was studied for evidence of neurological disorder. Six out of 892 patients were found who had neuromuscular disease related to the conduction disturbance. In four patients, cardiac involvement appeared selectively to affect the conducting tissues. Three of these patients had a scapuloperoneal syndrome, the fourth, the oculocraniosomatic syndrome. In the remaining two patients, one with limb girdle dystrophy and the other with dystrophia myotonica, cardiomyopathy was present in addition to the conduction disturbance.

摘要

对一大组慢性心脏传导阻滞患者进行了神经系统疾病证据的研究。在892例患者中,发现6例患有与传导障碍相关的神经肌肉疾病。在4例患者中,心脏受累似乎选择性地影响传导组织。其中3例患者患有肩胛腓骨综合征,第4例患有眼颅躯体综合征。在其余2例患者中,1例患有肢带型肌营养不良,另1例患有强直性肌营养不良,除传导障碍外还存在心肌病。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/accd/492351/af87c9b3f708/jnnpsyc00168-0059-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/accd/492351/af87c9b3f708/jnnpsyc00168-0059-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/accd/492351/af87c9b3f708/jnnpsyc00168-0059-a.jpg

相似文献

1
Neurological associations of chronic heart block.慢性心脏传导阻滞的神经学关联
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2
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引用本文的文献

1
Ophthalmoplegia-plus.眼肌麻痹加征
Doc Ophthalmol. 1981 Nov;51(4):373-82. doi: 10.1007/BF00143339.
2
Mitochondrial cytopathy. A multisystem disorder with ragged red fibres on muscle biopsy.线粒体细胞病。一种多系统疾病,肌肉活检可见破碎红纤维。
Arch Dis Child. 1981 Oct;56(10):741-52. doi: 10.1136/adc.56.10.741.
3
Kearns syndrome: a heterogeneous group of disorders with CPEO, or a nosological entity?卡恩斯综合征:一组伴有慢性进行性眼外肌麻痹的异质性疾病,还是一种疾病分类实体?

本文引用的文献

1
ETIOLOGY AND PATHOLOGY OF BILATERAL BUNDLE BRANCH BLOCK IN RELATION TO COMPLETE HEART BLOCK.双侧束支传导阻滞与完全性心脏传导阻滞相关的病因学和病理学
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Ophthalmoplegia plus. The neurodegenerative disorders associated with progressive external ophthalmoplegia.眼肌麻痹叠加症。与进行性眼外肌麻痹相关的神经退行性疾病。
Arch Neurol. 1968 Jun;18(6):654-74. doi: 10.1001/archneur.1968.00470360076008.
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[New type of recessive X-linked muscular dystrophy: scapulo-humeral-distal muscular dystrophy with early contractures and cardiac arrhythmias].
Doc Ophthalmol. 1982 Jan 29;52(3-4):207-25. doi: 10.1007/BF01675852.
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Congestive heart failure due to mitochondrial cardiomyopathy in Kearns-Sayre syndrome.卡恩斯-塞尔综合征中线粒体心肌病所致的充血性心力衰竭。
Klin Wochenschr. 1987 May 15;65(10):480-6. doi: 10.1007/BF01712843.
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Neurological aspects of sinoatrial heart block.窦房结性心脏传导阻滞的神经学方面
J Neurol Neurosurg Psychiatry. 1976 Jun;39(6):576-80. doi: 10.1136/jnnp.39.6.576.
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Skeletal muscle pathology in chronic heart block.慢性心脏传导阻滞中的骨骼肌病理学
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Ophthalmoplegia plus with morphological and chemical studies of cerebellar and muscle tissue.
J Neurol Sci. 1973 May;19(1):37-44. doi: 10.1016/0022-510x(73)90054-3.
5
The Kearns-Shy syndrome. A multisystem disease with mitochondrial abnormality demonstrated in skeletal muscle and skin.卡恩斯-谢综合征。一种多系统疾病,在骨骼肌和皮肤中表现出线粒体异常。
J Neurol Sci. 1973 Jun;19(2):133-51. doi: 10.1016/0022-510x(73)90158-5.
6
Scapuloperoneal muscular atrophy with cardiopathy. An X-linked recessive trait.伴有心肌病的肩胛腓骨肌萎缩症。一种X连锁隐性性状。
Arch Neurol. 1973 Jan;28(1):55-9. doi: 10.1001/archneur.1973.00490190073010.
7
Scapuloperoneal dystrophy associated with neurogenic changes.伴有神经源性改变的肩胛腓骨肌营养不良症
J Neurol Sci. 1974 Dec;23(4):575-83. doi: 10.1016/0022-510x(74)90029-x.
8
Oculocraniosomatic neuromuscular disease with "ragged-red" fibers.伴有“破碎红”纤维的眼颅体神经肌肉疾病
Arch Neurol. 1972 Mar;26(3):193-211. doi: 10.1001/archneur.1972.00490090019001.
9
X-linked scapuloperoneal syndrome.X连锁肩胛腓骨综合征
J Neurol Neurosurg Psychiatry. 1972 Apr;35(2):208-15. doi: 10.1136/jnnp.35.2.208.
10
Adult onset scapuloperoneal myopathy.成人起病性肩胛腓骨肌病
J Neurol Neurosurg Psychiatry. 1975 Oct;38(10):1008-15. doi: 10.1136/jnnp.38.10.1008.