Rusin L J, Harrell E R
Arch Dermatol. 1976 Aug;112(8):1135-8.
The association between congenital large-vessel arteriovenous (AV) fistulae of the extremities with Kaposiform acroangiomatosis is well established. Based on pathogenetic considerations, it is likely that many benign, cutaneous angiomatoses represent minute or microscopic AV fistulae. Combined large vessel and small vessel congenital AV fistulae of the extremity would result in the previously mentioned syndrome.
四肢先天性大血管动静脉（AV）瘘与卡波西样血管内皮瘤病之间的关联已得到充分证实。基于发病机制的考虑，许多良性皮肤血管瘤可能代表微小或显微镜下可见的AV瘘。肢体合并大血管和小血管先天性AV瘘会导致上述综合征。
