Han D S, Kim J B, Lee O Y, Sohn J H, Park K N, Park C K
Department of Internal Medicine, Radiology Hanyang University Kuri Hospital, Korea.
Korean J Intern Med. 1998 Feb;13(1):72-5. doi: 10.3904/kjim.1998.13.1.72.
Behçet's syndrome is a multi-systemic and chronic disorder that affects many organs. It has been suggested that the diagnosis was based on the presence of the 'major' and 'minor' clinical criteria. When thromobophlebitis, arthritis, central nervous system or gastrointestinal lesions are also present. Behçet's syndrome will be thought to be present in the appropriate geographic area. We report a case of superior vena cava syndrome caused by Behçet's disease in a 40-year-old man with recurrent oral aphthous ulcers and skin rashes on the anterior chest wall. There were multiple thrombosis of the superior vena cava, innominate and subclavian veins. This patient also had a solitary cecal ulcer with an ileocecal fistula and downhill varix. The chest CT, veno-cavography, pulmonary angiography and colon study were taken and follow-up was performed.
白塞病是一种影响多个器官的多系统慢性疾病。有人提出,诊断基于“主要”和“次要”临床标准的存在。当同时存在血栓性静脉炎、关节炎、中枢神经系统或胃肠道病变时,在适当的地理区域会认为存在白塞病。我们报告一例由白塞病引起的上腔静脉综合征病例,患者为一名40岁男性,有复发性口腔溃疡和前胸壁皮疹。上腔静脉、无名静脉和锁骨下静脉有多处血栓形成。该患者还患有一个孤立的盲肠溃疡并伴有回盲部瘘管和下行性静脉曲张。进行了胸部CT、静脉造影、肺血管造影和结肠检查并进行了随访。