Laloyaux P, Veyckemans F, Van Dyck M
Department of Anesthesiology, Cliniques Universitaires St Luc, Catholic University of Louvain Medical School, Brussels, Belgium.
Paediatr Anaesth. 1998;8(2):163-6. doi: 10.1046/j.1460-9592.1998.00687.x.
Cantrell's pentalogy (CP) is a rare congenital syndrome combining a defect of the supraumbilical abdominal wall, the agenesis of the lower part of the sternum and of the anterior portion of the diaphragm, the absence of the diaphragmatic part of the pericardium, and a cardiac malformation. It was first described by Cantrell in 1958 (1,2). We report the case of a prematurely born infant with CP and Wolff-Parkinson-White (WPW) syndrome who required surgery first for bilateral inguinal hernia repair and later for Blalock-Taussig shunt. During these two procedures, our anaesthetic plan was to preserve the fragile equilibrium of both the pulmonary and the cardiovascular systems.
坎特雷尔五联症(CP)是一种罕见的先天性综合征,合并脐上腹壁缺损、胸骨下部和膈肌前部发育不全、心包膈部缺如以及心脏畸形。它于1958年由坎特雷尔首次描述(1,2)。我们报告了一例患有CP和 Wolff-Parkinson-White(WPW)综合征的早产儿病例,该患儿首先需要进行双侧腹股沟疝修补手术,之后进行布莱洛克-陶西格分流术。在这两个手术过程中,我们的麻醉计划是维持脆弱的肺和心血管系统平衡。