Diamond H M, Lyon E S, Hui N T, De Pauw A P
J Urol. 1976 Oct;116(4):519-21. doi: 10.1016/s0022-5347(17)58890-4.
The thirty-second case of leiomyosarcoma of the inferior vena cava and the twelfth resectable patient in the series is presented. A review of the literature demonstrates a marked female preponderance (5 to 1). The most common presenting symptom is right abdominal pain and a palpable mass. The different surgical problems generated by the involved segment of the cava are discussed. Noteworthy is the high incidence of Budd-Chiari syndrome owing to hepatic vein obstruction with involvement of the upper third of the cava in the postmortem cases. An argument is developed for debulking the tumor for palliation when it is not completely removable.
本文报告了下腔静脉平滑肌肉瘤的第32例病例,也是该系列中第12例可切除的患者。文献回顾显示女性明显占优势(5比1)。最常见的症状是右腹痛和可触及的肿块。讨论了下腔静脉受累节段所产生的不同手术问题。值得注意的是,在尸检病例中,由于肝静脉阻塞且下腔静脉上三分之一受累,布加综合征的发生率很高。对于肿瘤无法完全切除时为缓解症状而行减瘤手术提出了依据。