Matsumoto S, Kang Y, Sato S, Kawakami Y, Oda Y, Araki M, Kawamura J, Uchida H
Department of Neurosurgery, Kobe City General Hospital, Kobe, Japan.
J Neurosurg. 1998 May;88(5):890-4. doi: 10.3171/jns.1998.88.5.0890.
Meningeal melanocytoma is a benign melanocytic tumor that originates most frequently from the melanocytes in the posterior fossa or along the spinal cord. This tumor generally occurs as an extraaxial mass that compresses adjacent neural structures to produce various neurological signs. The authors describe an unusual case in which a patient with a meningeal melanocytoma located at the thoracic spinal cord presented with superficial siderosis of the central nervous system (CNS). Extensive neuroradiological studies identified the presence of a spinal cord tumor, and postsurgical histological examination revealed the meningeal melanocytoma as a bleeding source. After surgery, lumbar puncture demonstrated normalization of the patient's cerebrospinal fluid; however, no neurological improvement occurred. The neurological deficits seem irreversible. Meningeal melanocytoma is biologically benign and can be cured by complete surgical resection; therefore, this tumor should be included in the differential diagnosis of pigmented lesions of the CNS. The authors reviewed 14 cases of well-documented meningeal melanocytoma in the literature and discuss the clinical, radiological, and pathological features of the present case to emphasize the importance of early diagnosis and identification of the source of bleeding in patients with superficial siderosis.
脑膜黑素细胞瘤是一种良性黑素细胞肿瘤,最常起源于后颅窝或脊髓的黑素细胞。该肿瘤通常表现为轴外肿块,压迫相邻神经结构,产生各种神经症状。作者描述了一例不寻常的病例,一名位于胸段脊髓的脑膜黑素细胞瘤患者出现中枢神经系统(CNS)浅表性含铁血黄素沉着症。广泛的神经放射学检查发现了脊髓肿瘤,术后组织学检查显示脑膜黑素细胞瘤为出血源。手术后,腰椎穿刺显示患者脑脊液恢复正常;然而,神经功能并未改善。神经功能缺损似乎不可逆转。脑膜黑素细胞瘤在生物学上是良性的,可通过完整的手术切除治愈;因此,该肿瘤应列入中枢神经系统色素沉着病变的鉴别诊断。作者回顾了文献中14例有充分记录的脑膜黑素细胞瘤病例,并讨论了本例的临床、放射学和病理学特征,以强调早期诊断和识别浅表性含铁血黄素沉着症患者出血源的重要性。