Ryu Sung Mo, Kim Eun-Sang, Kim Seung-Kook, Lee Sun-Ho, Eoh Whan
Department of Neurosurgery, Samsung Medical Center, Sungkyunkwan University School of Medicine, Seoul, Korea.
Korean J Spine. 2016 Jun;13(2):83-6. doi: 10.14245/kjs.2016.13.2.83. Epub 2016 Jun 30.
Superficial siderosis of the central nervous system(SSCNS) is a rare disease characterized by hemosiderin deposition on the surface of the central nervous system. We report a case of SSCNS originating from the thoracic spine, presenting with neurological deficits including, sensorineuronal hearing loss, ataxia, and corticospinal and dorsal column tract signs. The patient underwent dural repair with an artificial dural patch. Clinical findings were elicited by neurological examination, imaging studies, and intraoperative findings, and these were addressed through literature review.
中枢神经系统表面铁沉积症(SSCNS)是一种罕见疾病,其特征为含铁血黄素沉积于中枢神经系统表面。我们报告一例源自胸椎的SSCNS病例,该病例表现出神经功能缺损,包括感觉神经性听力丧失、共济失调以及皮质脊髓束和后索体征。患者接受了人工硬脑膜补片进行的硬脑膜修复术。通过神经学检查、影像学研究及术中所见得出临床结果,并通过文献回顾对这些结果进行了分析。