Guimarães P, Teixeira F, Morais L, Alvares S
Unidade de Cardiologia Pediátrica, Hospital de Crianças Maria Pia.
Rev Port Cardiol. 1998 Jan;17(1):89-92.
Hypertrophic cardiomyopathy is rare in neonates. The causes include metabolic disease, maternal diabetes, dexamethasone therapy in premature newborns for bronchopulmonary dysplasia and idiopathic hypertrophic cardiomyopathy. The authors present a case report regarding a neonate with transient hypertrophic cardiomyopathy, after acute fetal distress. Signs of congestive cardiac failure appeared at day 1. Echocardiography showed signs of mild pulmonary hypertension and normal ventricular wall thickness. Echocardiography on day 2 showed hypertrophy of myocardial walls affecting first the right ventricular anterior wall and the interventricular septum, followed by the left ventricular posterior wall. With therapy, clinical improvement was noted on day 4. The ventricular wall thickness was almost normal at three weeks. The authors alert physicians to the importance of echocardiographic examination of these neonates.
肥厚型心肌病在新生儿中较为罕见。病因包括代谢性疾病、母亲糖尿病、早产新生儿因支气管肺发育不良接受地塞米松治疗以及特发性肥厚型心肌病。作者报告了一例急性胎儿窘迫后出现短暂性肥厚型心肌病的新生儿病例。充血性心力衰竭症状在第1天出现。超声心动图显示轻度肺动脉高压及心室壁厚度正常。第2天的超声心动图显示心肌壁肥厚，首先累及右心室前壁和室间隔，随后是左心室后壁。经过治疗，第4天临床症状有所改善。三周时心室壁厚度几乎恢复正常。作者提醒医生对这些新生儿进行超声心动图检查的重要性。
