Lapina S P
Vestn Khir Im I I Grek. 1976 Apr;116(4):117-22.
In the paper, an experience with surgical treatment of 67 children suffering inherited spherocytosis is summarized. In most patients the first signs of the disease appeared in early age. It is concluded that splenectomy is indicated in all children with inherited spherocytosis irrespective of the form of the disease at the age from 3 to 5 years. In a grave course and the appearance of signs of functional hepatic insufficiency the operation should be accomplished as earlier as posisble.
本文总结了对67例遗传性球形红细胞增多症患儿的手术治疗经验。大多数患者在幼年时出现该病的最初症状。得出的结论是，所有遗传性球形红细胞增多症患儿，无论疾病类型如何，在3至5岁时均应行脾切除术。在病情严重且出现肝功能不全迹象时，手术应尽早进行。
