Cáp J
II. detská klinika Detskej fakultnej nemocnice s poliklinikou, Bratislava.
Cesk Pediatr. 1992 Oct;47(10):592-5.
The author investigated during a 15-year period 27 children with spherocytic haemolytic anaemia. In 20 children the disease was familial. The initial symptoms were jaundice and anaemia. In six children the disease was manifested by severe neonatal jaundice and in four an exsanguination transfusion was made. Of five older children three were at first treated for infectious hepatitis. The anaemic syndrome was in the foreground of the clinical picture in 16 children, incl. 10 where it was present already in infant age. In 24 children splenectomy was performed, usually after the age of 6 years. For prophylaxis of bacterial infection the splenectomized children were given penicillin preparations for a period of three years. The OPSI syndrome was not recorded.
作者在15年期间对27例球形红细胞溶血性贫血患儿进行了研究。其中20例患儿的疾病为家族性。初始症状为黄疸和贫血。6例患儿以严重的新生儿黄疸为表现，4例患儿进行了大量输血。在5例年龄较大的患儿中，3例最初被诊断为感染性肝炎。16例患儿的贫血综合征是临床表现的主要方面，其中10例在婴儿期就已出现。24例患儿接受了脾切除术，通常在6岁以后。为预防细菌感染，脾切除术后的患儿接受了三年的青霉素治疗。未记录到暴发性感染性脾切除术后感染综合征（OPSI）。
