Akashi T, Nagafuchi S, Anzai K, Kitamura D, Wang J, Taniuchi I, Niho Y, Watanabe T
First Department of Internal Medicine, Faculty of Medicine, Fukuoka University, Japan.
Immunology. 1998 Feb;93(2):238-48. doi: 10.1046/j.1365-2567.1998.00416.x.
It is known that lpr mice develop systemic lymphadenopathy and lupus erythematosus-like autoimmune disease that are associated with the accumulation of CD4- CD8- (double-negative; DN) CD3+ B220+ abnormal T cells as well as normal mature CD4+ or CD8+ single-positive (SP) CD3+ T cells. In order to clarify the role of B cells in the lymphoproliferation and autoimmunity of lpr mice, we created B-cell-deficient C57BL/6 (B6) lpr mice (B6lpr/lpr microMT/microMT) by crossing B6lpr/lpr mice with B6 microMT/microMT mice in which the B-cell development was arrested at pre-B stage owing to a targeted disruption of the immunoglobulin mu heavy-chain gene locus. In the B-cell-deficient B6-lpr mice, both lymphadenopathy and splenomegaly were markedly suppressed. Although the accumulation of both CD3+ B220- SP normal T cells and CD3+ B220+ DN abnormal T cells was inhibited in the B-cell-deficient lpr mice, the decrease in numbers of CD3+ B220- SP normal T cells occurred more strikingly than that of the CD3+ B220+ DN abnormal T cells. Glomerulonephritis did not develop in the B-cell-deficient lpr mice over 40 weeks. The present results indicate that the B cells thus play a crucial role in the extensive proliferation of normal CD3+ B220- mature SP T cells rather than the accumulation of abnormal DN T cells.
已知lpr小鼠会出现全身淋巴结病和狼疮样自身免疫性疾病,这与CD4 - CD8 -(双阴性;DN)CD3 + B220 +异常T细胞以及正常成熟的CD4 +或CD8 +单阳性(SP)CD3 + T细胞的积累有关。为了阐明B细胞在lpr小鼠淋巴细胞增殖和自身免疫中的作用,我们通过将B6lpr/lpr小鼠与B6 microMT/microMT小鼠杂交,创建了B细胞缺陷的C57BL/6(B6)lpr小鼠(B6lpr/lpr microMT/microMT),其中由于免疫球蛋白μ重链基因位点的靶向破坏,B细胞发育在pre - B阶段停滞。在B细胞缺陷的B6 - lpr小鼠中,淋巴结病和脾肿大均得到明显抑制。虽然在B细胞缺陷的lpr小鼠中,CD3 + B220 - SP正常T细胞和CD3 + B220 + DN异常T细胞的积累均受到抑制,但CD3 + B220 - SP正常T细胞数量的减少比CD3 + B220 + DN异常T细胞更显著。在40周以上的B细胞缺陷lpr小鼠中未发生肾小球肾炎。目前的结果表明,B细胞在正常CD3 + B220 -成熟SP T细胞的广泛增殖中起关键作用,而不是在异常DN T细胞的积累中起关键作用。