Nagata K, Iwasaki Y, Yokomura I, Ueda M, Hashimoto S, Mizobuchi K, Arimoto T, Nakagawa M
Second Department of Medicine, Kyoto Prefectural University of Medicine, Japan.
Nihon Kokyuki Gakkai Zasshi. 1998 Feb;36(2):171-5.
We report a case of Swyer-James syndrome with pneumothorax. A 20 year-old man was admitted to our hospital with dyspnea. Right pneumothorax was diagnosed by chest X-ray. He had a history of current pneumonia in childhood. After improvement of the pneumothorax, chest X-ray revealed hyperlucency of the right upper lung. Chest-CT revealed a low attenuation area and a cystic space in the right upper lobe. Xenon-133 clearance was delayed in ventilation scintigraphy. Bronchography showed cylindrical bronchiectasis in the proximal bronchi and poor filling of the peripheral bronchi in the right upper lobe. Pulmonary angiography showed a small right upper pulmonary artery. Swyer-James syndrome was diagnosed. The pneumothorax was probably caused by weakness of the cystic spaces.
我们报告一例伴有气胸的斯怀尔-詹姆斯综合征。一名20岁男性因呼吸困难入院。胸部X线检查诊断为右侧气胸。他童年时有患肺炎的病史。气胸病情好转后，胸部X线显示右上肺透亮度增加。胸部CT显示右上叶有一个低密度区和一个囊腔。通气闪烁扫描显示氙-133清除延迟。支气管造影显示近端支气管呈圆柱状扩张，右上叶外周支气管充盈不佳。肺血管造影显示右上肺动脉细小。诊断为斯怀尔-詹姆斯综合征。气胸可能是由囊腔壁薄弱所致。
