Sferopoulos N K, Anagnostopoulos D, Webb J K
Department of Paediatric Surgery, Aristotle University of Thessaloniki, Greece.
Eur Spine J. 1998;7(3):257-9. doi: 10.1007/s005860050069.
The case of a 2 1/2-year-old boy with diffuse cystic angiomatosis of bone is presented. No evidence of visceral involvement was recorded. The clinical, radiographic and histologic findings during the course of the disease process are discussed. At the age of 15 years the patient died of neurologic alterations developed due to massive osteolysis and collapse of the cervical spine, and severe dyspnoea, secondary to persistent bilateral pleural effusions.
本文报告了一例2岁半男孩患弥漫性骨囊性血管瘤病的病例。未记录到内脏受累的证据。讨论了疾病过程中的临床、影像学和组织学表现。患者15岁时死于因颈椎大量骨质溶解和塌陷导致的神经功能改变,以及因持续性双侧胸腔积液继发的严重呼吸困难。