Rivera I R, Moisés V A, Silva C C, Leal S B, Maluf M A, Andrade J L, Carvalho A C
Escola Paulista de Medicina--UNIFESP--São Paulo.
Arq Bras Cardiol. 1998 May;70(5):341-4. doi: 10.1590/s0066-782x1998000500007.
The origin of the right pulmonary artery from the ascending aorta is a rare cogenital anomaly, with very few reports in the literature. We describe two cases of this rare malformation, one of them, associated with interruption of the aortic arch (type B). In both cases, the diagnosis was made by two-dimensional echocardiography, with angiographic confirmation in one of them. The origin of the right pulmonary artery was close to the aortic valve, anomaly pathogenetically distinct from the type that arises close to the innominate artery.
右肺动脉起源于升主动脉是一种罕见的先天性异常,文献报道极少。我们描述了两例这种罕见的畸形病例,其中一例伴有主动脉弓中断(B型)。两例均通过二维超声心动图确诊,其中一例经血管造影证实。右肺动脉起源靠近主动脉瓣,在发病机制上与起源于无名动脉附近的类型不同。