Hilgard P, Oberholzer K, Meyer zum Büschenfelde K H, Hohenfellner R, Gerken G
I. Medizinische Klinik und Poliklinik, Johannes Gutenberg-Universität Mainz.
Dtsch Med Wochenschr. 1998 Jul 31;123(31-32):936-40. doi: 10.1055/s-2007-1024101.
Since the age of 19 a now 22-year-old man had complained of intermittent abdominal pain, irregular stools and paroxysmal tachycardia. The only preceding illness had been a single episode of iron-deficiency anemia. A laparoscopy, done 8 months after the onset of symptoms, had revealed an inflamed Meckel's diverticulum which was surgically removed. After transient improvement the symptoms recurred 5 months postoperatively. On admission to clarify the cause of the symptoms he had discrete abdominal pain on pressure, but physical examination was otherwise unremarkable.
Routine biochemical tests and endoscopy were normal. Abdominal computed tomography was suspicious of severe narrowing of the left renal artery by a crossing superior mesenteric artery. As a result the left testicular vein and the peripelvic venous network were markedly dilated by retrograde congestion, strongly suggesting the "nutcracker syndrome" of obstruction of the left renal vein. This diagnosis was confirmed by selective renal phlebography and pressure measurement.
The vascular anomaly was corrected surgically by reimplanting the left renal vein into the inferior vena cava 3-4 cm further caudally. The patients has been completely symptom-free since then.
The nutcracker-syndrome is a rare cause of hematuria. The coexistence of this anomaly with gastrointestinal symptoms has not been previously described, but it is likely that congestion of the splanchnic veins by obstruction of the left renal vein was at least partly responsible for them, in view of the postoperative relief.
一名现22岁男性自19岁起便主诉间歇性腹痛、大便不规律及阵发性心动过速。之前仅患过一次缺铁性贫血。症状出现8个月后进行了腹腔镜检查,发现梅克尔憩室发炎,遂将其手术切除。术后短暂好转后,症状在术后5个月复发。入院以明确症状原因时,他在按压时有轻微腹痛,但体格检查其他方面无异常。
常规生化检查及内镜检查均正常。腹部计算机断层扫描怀疑肠系膜上动脉交叉导致左肾动脉严重狭窄。结果,左睾丸静脉及肾周静脉网因逆行性充血而明显扩张,强烈提示左肾静脉受压的“胡桃夹综合征”。选择性肾静脉造影及压力测量证实了这一诊断。
通过将左肾静脉再植入下腔静脉尾侧3 - 4厘米处,手术纠正了血管异常。此后患者症状完全消失。
胡桃夹综合征是血尿的罕见病因。此前尚未描述过这种异常与胃肠道症状并存的情况,但鉴于术后症状缓解,左肾静脉阻塞导致的内脏静脉充血很可能至少部分导致了这些症状。