• 文献检索
  • 文档翻译
  • 深度研究
  • 学术资讯
  • Suppr Zotero 插件Zotero 插件
  • 邀请有礼
  • 套餐&价格
  • 历史记录
应用&插件
Suppr Zotero 插件Zotero 插件浏览器插件Mac 客户端Windows 客户端微信小程序
定价
高级版会员购买积分包购买API积分包
服务
文献检索文档翻译深度研究API 文档MCP 服务
关于我们
关于 Suppr公司介绍联系我们用户协议隐私条款
关注我们

Suppr 超能文献

核心技术专利:CN118964589B侵权必究
粤ICP备2023148730 号-1Suppr @ 2026

文献检索

告别复杂PubMed语法,用中文像聊天一样搜索,搜遍4000万医学文献。AI智能推荐,让科研检索更轻松。

立即免费搜索

文件翻译

保留排版,准确专业,支持PDF/Word/PPT等文件格式,支持 12+语言互译。

免费翻译文档

深度研究

AI帮你快速写综述,25分钟生成高质量综述,智能提取关键信息,辅助科研写作。

立即免费体验

先天性皮肤缺损作为存活双胎的并发症。先天性皮肤发育不全和新生儿前臂Volkmann缺血性挛缩。

Congenital cutaneous defects as complications in surviving co-twins. Aplasia cutis congenita and neonatal volkmann ischemic contracture of the forearm.

作者信息

Léauté-Labrèze C, Depaire-Duclos F, Sarlangue J, Fontan D, Sandler B, Maleville J, Taïeb A

机构信息

Pediatric Dermatology Unit, Hôpital Pellegrin-Enfants, Bordeaux, France.

出版信息

Arch Dermatol. 1998 Sep;134(9):1121-4. doi: 10.1001/archderm.134.9.1121.

DOI:10.1001/archderm.134.9.1121
PMID:9762026
Abstract

BACKGROUND

During twin pregnancies, several complications may result in the death of a co-twin depending on the date of death. We describe herein 2 infant survivors of monozygotic twin pairs with 2 distinct possible complications: a aplasia cutis congenita and Volkmann ischemic contracture.

OBSERVATIONS

One infant had extensive aplasia cutis congenita with an associated monozygotic co-twin who died at 3 months of gestation, and the other child had a localized arm defect due to Volkmann ischemic contracture and brain damage, with a co-twin who died at approximately 6 weeks of gestation.

CONCLUSIONS

Congenital cutaneous defects may result in the death of a co-twin. The most common of these defects is aplasia cutis congenita associated with a fetus papyraceus or a dead fetus related to ischemic/thrombotic events in the placenta and fetus. Volkmann ischemic contracture is rare in the newborn but can cause neonatal cutaneous defects. The cause of Volkmann ischemic contracture in newborns is unknown; however, our second observation suggests the possible role of a dead fetus.

摘要

背景

在双胎妊娠期间,根据死亡时间的不同,多种并发症可能导致其中一个胎儿死亡。我们在此描述了2例单卵双胎的婴儿幸存者,他们出现了2种不同的可能并发症:先天性皮肤发育不全和福克曼缺血性挛缩。

观察结果

一名婴儿患有广泛的先天性皮肤发育不全,其单卵双胎在妊娠3个月时死亡;另一名儿童因福克曼缺血性挛缩和脑损伤出现局部手臂缺陷,其双胎在妊娠约6周时死亡。

结论

先天性皮肤缺陷可能导致双胎中的一个胎儿死亡。这些缺陷中最常见的是与纸样胎儿或与胎盘和胎儿缺血/血栓形成事件相关的死胎相关的先天性皮肤发育不全。福克曼缺血性挛缩在新生儿中罕见,但可导致新生儿皮肤缺陷。新生儿福克曼缺血性挛缩的病因尚不清楚;然而,我们的第二个观察结果提示了死胎可能起到的作用。

相似文献

1
Congenital cutaneous defects as complications in surviving co-twins. Aplasia cutis congenita and neonatal volkmann ischemic contracture of the forearm.先天性皮肤缺损作为存活双胎的并发症。先天性皮肤发育不全和新生儿前臂Volkmann缺血性挛缩。
Arch Dermatol. 1998 Sep;134(9):1121-4. doi: 10.1001/archderm.134.9.1121.
2
Aplasia Cutis Congenita with Ischemic Cortical Change and Normal Array Cytogenetic Analysis with a Fetus Papyraceus Twin.先天性皮肤发育不全伴缺血性皮质改变及纸样胎儿双胎的正常核型细胞遗传学分析
Fetal Pediatr Pathol. 2018 Aug;37(4):276-281. doi: 10.1080/15513815.2018.1483453. Epub 2018 Oct 1.
3
Aplasia cutis congenita in surviving co-twins: four unrelated cases.存活双胞胎中的先天性皮肤发育不全:四例非亲缘关系病例。
Pediatr Dermatol. 2001 Nov-Dec;18(6):511-5. doi: 10.1046/j.1525-1470.2001.1861998.x.
4
Aplasia cutis congenita with fetus papyraceus: report and review of the literature.先天性皮肤发育不全伴纸样胎儿:报告及文献复习。
Int J Dermatol. 2012 Dec;51(12):1419-26. doi: 10.1111/j.1365-4632.2012.05545.x.
5
A case of aplasia cutis congenita in dizygotic twins.一例双卵双胎先天性皮肤发育不全病例。
J Perinatol. 1993 Jan-Feb;13(1):22-7.
6
Fetus papyraceus: congenital pulmonary anomalies associated with congenital aplasia cutis on the surviving twin.纸样胎儿:存活双胎中与先天性皮肤发育不全相关的先天性肺部异常。
Pediatr Dermatol. 2013 Nov-Dec;30(6):e143-5. doi: 10.1111/pde.12096. Epub 2013 Feb 26.
7
Congenital Volkmann syndrome and aplasia cutis of the forearm: a challenging differential diagnosis.先天性 Volkmann 综合征和前臂皮肤发育不全:具有挑战性的鉴别诊断。
JAMA Dermatol. 2014 Sep;150(9):978-80. doi: 10.1001/jamadermatol.2014.111.
8
Symmetric aplasia cutis congenita associated with fetus papyraceus: report of two cases.与纸样胎儿相关的对称性先天性皮肤发育不全:两例报告
Pediatr Dermatol. 2011 Jul-Aug;28(4):467-9. doi: 10.1111/j.1525-1470.2011.01314.x. Epub 2011 Mar 25.
9
Coexistence of aplasia cutis congenita, faun tail nevus and fetus papyraceus.先天性皮肤发育不全、兽尾痣和纸样胎儿并存。
J Dermatol Case Rep. 2013 Sep 30;7(3):93-6. doi: 10.3315/jdcr.2013.1148. eCollection 2013.
10
Multiple aplasia cutis congenita type V and fetus papyraceous: a case report and review of the literature.V型多发性先天性皮肤发育不全与压扁胎:1例病例报告及文献复习
J Med Case Rep. 2021 Mar 4;15(1):110. doi: 10.1186/s13256-021-02662-3.

引用本文的文献

1
Neonatal Compartment Syndrome and Compound Presentation at Birth.新生儿骨筋膜室综合征及出生时的复合表现
J Hand Surg Glob Online. 2020 May 8;2(3):166-170. doi: 10.1016/j.jhsg.2020.04.001. eCollection 2020 May.
2
A practical approach to the evaluation and treatment of an infant with aplasia cutis congenita.先天性皮肤发育不全婴儿评估与治疗的实用方法。
J Perinatol. 2018 Feb;38(2):110-117. doi: 10.1038/jp.2017.142. Epub 2017 Oct 19.
3
Neonatal volkmann ischemic contracture: case report and review of literature.新生儿福克曼缺血性挛缩:病例报告及文献综述
AJP Rep. 2014 Nov;4(2):e77-80. doi: 10.1055/s-0034-1382257. Epub 2014 Jun 24.
4
Volkmann ischemic contracture in a newborn.新生儿Volkmann缺血性挛缩
BMJ Case Rep. 2011 Sep 26;2011:bcr0520114201. doi: 10.1136/bcr.05.2011.4201.
5
Aplasia cutis in association with a triplet pregnancy and fetus papyraceus.皮肤发育不全合并三胎妊娠及纸样胎儿。
BMJ Case Rep. 2009;2009:bcr2007126110. doi: 10.1136/bcr.2007.126110. Epub 2009 Feb 16.