Fray A E, Ince P G, Banner S J, Milton I D, Usher P A, Cookson M R, Shaw P J
Department of Neurology, University of Newcastle upon Tyne, UK.
Eur J Neurosci. 1998 Aug;10(8):2481-9. doi: 10.1046/j.1460-9568.1998.00273.x.
Emerging evidence suggests that a disturbance of the glutamate neurotransmitter system may be a contributory factor to motor neuron injury in motor neuron disease. Previous autoradiographic and immunoblotting studies have suggested that there may be reduced expression of glutamate transporter proteins in pathologically affected areas of the CNS in motor neuron disease. This study further explores the possible alteration in expression of the excitatory amino acid transporter protein EAAT2 in MND, by examining the protein expression in situ, in frozen sections, using immunohistochemistry. The aim of the study was to compare the distribution and density of EAAT2 in the motor cortex and spinal cord of MND cases (n = 16) compared with neurologically normal controls (n = 12), matched for relevant parameters. A novel, previously characterized, monoclonal antibody to EAAT2 was employed. EAAT2 immunoreactivity in motor neuron disease and control cases was compared using relative optical density measurements generated by computerized image analysis. In the motor cortex, EAAT2 immunoreactivity was laminated comprising a superficial intense band (corresponding to layers 1 and 2); a paler middle band (layer 3 and part of 5) and a more intense deep layer (layers 5 and 6). In the spinal cord, the ventral horn showed strong immunoreactivity with dense perisomatic staining around motor neuron cell bodies, the substantia gelatinosa showed moderate diffuse staining and the intermediate spinal laminae showed weak staining. This general pattern of immunoreactivity was preserved in the motor neuron disease cases. However, in the motor neuron disease cases compared with controls, the optical density values for EAAT2 immunoreactivity were significantly reduced in all grey matter regions of the lumbar spinal cord (P < 0.001) and were increased in the middle laminae of the motor cortex (P < 0.05). This study indicates that glutamate transporter pathology in motor neuron disease may be a more complex phenomenon than previously recognized.
新出现的证据表明,谷氨酸神经递质系统紊乱可能是运动神经元病中运动神经元损伤的一个促成因素。先前的放射自显影和免疫印迹研究表明,在运动神经元病中枢神经系统的病理受累区域,谷氨酸转运蛋白的表达可能会降低。本研究通过免疫组织化学检查冰冻切片中兴奋性氨基酸转运蛋白EAAT2的原位蛋白表达,进一步探讨运动神经元病中EAAT2表达的可能变化。该研究的目的是比较16例运动神经元病患者与12例神经功能正常对照者(根据相关参数匹配)的运动皮质和脊髓中EAAT2的分布和密度。使用了一种针对EAAT2的新型、先前已鉴定的单克隆抗体。通过计算机图像分析生成的相对光密度测量值,比较了运动神经元病和对照病例中EAAT2的免疫反应性。在运动皮质中,EAAT2免疫反应性呈分层分布,包括一个浅表密集带(对应于第1和第2层);一个较淡的中间带(第3层和第5层的一部分)和一个较强的深层带(第5和第6层)。在脊髓中,腹角显示出强烈的免疫反应性,运动神经元细胞体周围有密集的胞体周围染色,胶状质显示中度弥漫性染色,脊髓中间层显示弱阳性。这种免疫反应性的总体模式在运动神经元病病例中得以保留。然而,与对照相比,运动神经元病病例中,腰段脊髓所有灰质区域EAAT2免疫反应性的光密度值显著降低(P<0.001),而运动皮质中间层的光密度值升高(P<0.05)。这项研究表明,运动神经元病中的谷氨酸转运蛋白病理可能是一个比先前认识到的更为复杂的现象。