Disdier P, Weiller P J
Service de médecine interne, Hôpital de la Timone, Marseille.
Rev Prat. 1998 Mar 15;48(6):626-31.
Antiphospholipid syndrome is characterized by thromboses, fetal losses and antiphospholipid antibodies. This group of antibodies includes lupus anticoagulant, false positive syphilitic reaction, anionic (such as anticardiolipin) and neutral phospholipids antibodies, and anti-phospholipid/cofactors antibodies (such as anti-beta 2-glycoprotein 1). Dominant manifestations are recurrent thrombophlebitis and pulmonary embolism, arterial occlusive disease of young people, obstetrical complications such as fetal losses, livedo, and thrombocytopenia. Warfarin is presently the main treatment.
抗磷脂综合征的特征为血栓形成、胎儿丢失和抗磷脂抗体。这类抗体包括狼疮抗凝物、梅毒反应假阳性、阴离子(如抗心磷脂)和中性磷脂抗体,以及抗磷脂/辅因子抗体(如抗β2糖蛋白1)。主要表现为复发性血栓性静脉炎和肺栓塞、年轻人的动脉闭塞性疾病、诸如胎儿丢失等产科并发症、网状青斑和血小板减少症。华法林目前是主要治疗药物。