Al-Bassam A, Sheikh M A, Al-Smayer S, Al-Boukai A, Al-Damegh S
Department of Surgery, King Khalid University Hospital, Riyadh, Kingdom of Saudi Arabia.
J Pediatr Surg. 1998 Oct;33(10):1550-3. doi: 10.1016/s0022-3468(98)90496-1.
Congenital H-type anourethral fistula with severe urethral hypoplasia and normal anus is an extremely rare variant of anorectal malformations among boys. The authors report a case of a 5-year-old boy who underwent successful management of severe urethral hypoplasia with progressive augmentation by dilating urethra anterior gently and achieving a functionally normal urethra with minimal morbidity. H-type anourethral fistula was excised subsequently through anterior perianal approach.
先天性H型无尿道瘘合并严重尿道发育不全且肛门正常是男孩肛门直肠畸形中极为罕见的一种变异类型。作者报告了一例5岁男孩的病例,该男孩通过轻柔扩张前尿道进行渐进性扩张,成功治疗了严重尿道发育不全,最终获得了功能正常且并发症极少的尿道。随后通过肛周前路切除了H型无尿道瘘。