Weng K P, Chio Y H, Huang Y Y, Sung P K, Hsieh K S, Choong C S
Department of Pediatrics, Veterans General Hospital-Kaohsiung, Taiwan.
Zhonghua Min Guo Xiao Er Ke Yi Xue Hui Za Zhi. 1998 Sep-Oct;39(5):339-41.
Multicystic dysplastic kidney (MCDK) is a common cause of abdominal mass in neonates. It is frequently associated with malformation of the contralateral kidney, such as ureteropelvic obstruction, etc. Because MCDK is usually functionless, it is important to evaluate the condition of the contralateral kidney. The presence of severe obstruction in the contralateral ureteropelvic junction is life-threatening and prompt treatment should be made to preserve the remaining renal function. We report on a neonate with left MCDK and contralateral ureteropelvic obstruction, presenting as anuria after birth, and also we review the literature.
多囊性发育不良肾(MCDK)是新生儿腹部肿块的常见原因。它常与对侧肾脏畸形相关,如输尿管肾盂梗阻等。由于MCDK通常无功能,评估对侧肾脏状况很重要。对侧输尿管肾盂连接处存在严重梗阻会危及生命,应立即进行治疗以保留剩余肾功能。我们报告一例患有左侧MCDK和对侧输尿管肾盂梗阻的新生儿,出生后表现为无尿,同时我们也复习相关文献。