Maconi G, Cristaldi M, Vago L, Rovati M, Elli M, Sampietro G M, Nebuloni E, Sainaghi M, Taschieri A M, Bianchi Porro G
Gastrointestinal Unit, Luigi Sacco University Hospital, Milano, Italy.
Hepatogastroenterology. 1998 Sep-Oct;45(23):1663-6.
Primary mesenteric fibromatosis is a rare, histologically benign, pathology which is characterized by fibrous proliferation in the mesentery and made more serious by biological malignancy as it has a high inclination towards involving the visceral abdominal structures in its growth. While the cases reported in the literature describe the attempts to cure and reduce the tumor growth, this report describes the clinical, ultrasonographic and tomographic features during the natural growth rate of a case of inoperable primary mesenteric fibromatosis during a 20 month follow-up.
原发性肠系膜纤维瘤病是一种罕见的、组织学上为良性的病变，其特征是肠系膜纤维组织增生，由于其在生长过程中极易累及腹部内脏结构，具有生物学恶性倾向，病情更为严重。虽然文献报道的病例描述了治疗及减少肿瘤生长的尝试，但本报告描述了一例无法手术切除的原发性肠系膜纤维瘤病在20个月随访期间自然生长速度下的临床、超声及断层扫描特征。
