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以急性腹痛为主要症状的德戈斯病(恶性萎缩性丘疹病)。

Acute abdominal pain as a leading symptom for Degos' disease (malignant atrophic papulosis).

作者信息

Lankisch M R, Johst P, Scolapio J S, Fleming C R

机构信息

Division of Gastroenterology, Mayo Clinic Jacksonville, Florida, USA.

出版信息

Am J Gastroenterol. 1999 Apr;94(4):1098-9. doi: 10.1111/j.1572-0241.1999.1022_a.x.

Abstract

We report a case of a 16-yr-old white female patient with acute abdominal pain due to visceral involvement of Degos' disease that required extensive small bowel resection. Skin manifestations of her disease had been present for 2 yr before the correct diagnosis. She died as a result of central nervous system involvement from Degos' disease.

摘要

我们报告一例16岁白人女性患者,因德戈斯病累及内脏导致急性腹痛,需要广泛切除小肠。在正确诊断前,其疾病的皮肤表现已出现2年。她因德戈斯病累及中枢神经系统而死亡。

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