Erb-Gremillet S, Gunther M, Amiaux F, Parache R M
Service d'Anatomie et de Cytologie Pathologiques, Centre Alexis-Vautrin (CRLCC), Vandaeuvre-lès-Nancy.
Ann Pathol. 1999 Apr;19(2):124-7.
Breast-like carcinomas of the vulva is a rare finding. Only 11 cases are reported in the literature. This article reports a painful tumor of the left vulvar labia in a 62 year-old woman. Excisional biopsy showed an infiltrating adenocarcinoma, histologically similar to a breast tumor with positive hormonal receptors. The origin of this tumor, ectopic mammary tissue or specific adnexal genito-anal gland, is discussed. From data of the literature, we offer guidelines for diagnosis, treatment and origin of this rare tumor.
外阴乳腺样癌是一种罕见的病症。文献中仅报道了11例。本文报告了一名62岁女性左侧外阴唇的疼痛性肿瘤。切除活检显示为浸润性腺癌,组织学上类似于具有阳性激素受体的乳腺肿瘤。讨论了该肿瘤的起源,即异位乳腺组织或特定的生殖附属腺。根据文献数据,我们提供了关于这种罕见肿瘤的诊断、治疗和起源的指导原则。