背侧胰腺完全缺如。

Complete agenesis of the dorsal pancreas.

作者信息

Fukuoka K, Ajiki T, Yamamoto M, Fujiwara H, Onoyama H, Fujita T, Katayama N, Mizuguchi K, Ikuta H, Kuroda Y, Hanioka K

机构信息

First Department of Surgery, Kobe University School of Medicine, 7-5-2 Kusunoki-cho, Chuo-ku, Kobe 650-0017, Japan.

出版信息

J Hepatobiliary Pancreat Surg. 1999;6(1):94-7. doi: 10.1007/s005340050090.

DOI:10.1007/s005340050090

PMID:10436244

Abstract

Pancreatic anomalies are occasionally reported, but complete agenesis of the dorsal pancreas is extremely rare. We report a 47-year-old woman with complete agenesis of the dorsal pancreas. This patient initially presented with jaundice. Computed tomography did not reveal the pancreatic corpus or tail. Endoscopic retrograde cholangiopancreatography and magnetic resonance cholangiopancreatography did not visualize the dorsal pancreatic duct. Choledochojejunostomy was performed because she had obstructive jaundice. At laparotomy, there was an enlarged pancreatic head, but no distal pancreas was seen. Histological examination of the pancreatic biopsy specimen showed scattered islets of Langerhans in diffuse fibrosis, with destruction of the glandular parenchyma. This case was diagnosed as complete agenesis of the dorsal pancreas.

摘要

胰腺异常情况偶尔会有报道，但背侧胰腺完全缺如极为罕见。我们报告一例47岁背侧胰腺完全缺如的女性患者。该患者最初表现为黄疸。计算机断层扫描未显示胰体或胰尾。内镜逆行胰胆管造影和磁共振胰胆管造影均未显示背侧胰管。由于她患有梗阻性黄疸，故行胆总管空肠吻合术。剖腹手术时，可见胰头增大，但未见胰腺远端。胰腺活检标本的组织学检查显示，在弥漫性纤维化中有散在的胰岛，腺实质破坏。该病例被诊断为背侧胰腺完全缺如。