Schattenberg T, Pfannschmidt J, Herpel E, Schnabel P A, Mechtersheimer G, Dienemann H
Department of Thoracic Surgery, Heidelberg University, Heidelberg, Germany.
Thorac Cardiovasc Surg. 2007 Apr;55(3):199-200. doi: 10.1055/s-2006-924412.
Epitheloid hemangioendothelioma is a vascular tumour with an epitheloid appearance, originating from endothelial cells. Although it is a slow growing tumour, extensive pulmonary involvement, intrathoracic spread, and systemic spread have been documented. We present a case of epitheloid hemangioendothelioma of the lung in a patient with an initial diagnosis made by transthoracic biopsy. The prognosis is unpredictable, with life expectancy ranging from 1 to 20 years. There is no single effective treatment, though spontaneous regression and response to chemotherapy and interferon are reported. Our patient underwent pulmonary lobectomy of the right lower lobe and pulmonary wedge resection of the nodule located in the left lower lobe.
上皮样血管内皮瘤是一种具有上皮样外观的血管肿瘤,起源于内皮细胞。尽管它是一种生长缓慢的肿瘤,但已有广泛肺受累、胸腔内播散和全身播散的记录。我们报告一例经胸壁活检初步诊断为肺上皮样血管内皮瘤的患者。其预后不可预测,预期寿命为1至20年。虽然有自发消退以及对化疗和干扰素治疗有反应的报道,但尚无单一有效的治疗方法。我们的患者接受了右下肺叶切除术及左下肺结节的肺楔形切除术。