Frikha I, Masmoudi S, Hadjkacem A, Ghemissou N, Kolsi K, Khannous M, Karoui A, Sahnoun Y
Service de chirurgie thoracique et cardiovasculaire, CHU H.-Bourguiba, Tunisie.
Arch Mal Coeur Vaiss. 2000 Feb;93(2):195-8.
The aneurysm of the descending aorta complicating a pseudocoarctation, itself due to a congenital elongation with kinking of the aorta is a rare entity.
We report a case of aortic aneurysm discovered in a 72 years old woman without notable antecedents, which was referred for recurrent bronchitis. The X-ray showed a calcified opacity of the upper mediastinum, 5 cm of large. A thoracic CT-scan evoked the presence of a circulating sacciform aneurysm with calcified walls, developing on the final part of the aortic arch, which was with abnormally ascending way going up to the cervico-thoracic orifice and carrying out an aspect of aortic kinking. The assessment was complemented by a RMI as well as an aortic opacification. A thoracic scintigraphy showed an hypoperfusion of the left lung. The remainder of the cardiac assessment was normal. The patient was operated under femoro-femoral extracorporeal circulation through a left posterolateral thoracotomy of the 4th intercostal space. The examination showed a 7 cm diameter calcified aneurysm of the descending thoracic aorta complicating a tight stenosis in connection with an elongation and a kinking. The upper section of the aorta was shifted towards the pleural dome. The aortic section above aneurism was of normal size whereas the lower section was dilated. The aneurism was excised and a prosthetic graft was carried out. The surgery follow-up was marked by an hemodynamic stability, without neurological deficit. A ventilatory assistance was necessary during 5 days. Currently with 8 months follow-up, the patient goes well.
A prosthetic replacement in front of this type of aneurism is legitimate given the risk of the occurrence of complications secondary to the pseudocoarctation (arterial hypertension, aortic insufficiency) or to the aneurism itself, dissection or compression of vicinity (pulmonary artery).
降主动脉瘤合并假性缩窄,其本身是由于主动脉先天性延长并扭结,这种情况较为罕见。
我们报告一例在一名72岁无明显病史的女性中发现的主动脉瘤,该患者因反复支气管炎前来就诊。X线显示上纵隔有一个5厘米大的钙化阴影。胸部CT扫描显示在主动脉弓末端有一个壁钙化的囊状动脉瘤,呈异常上升走行直至颈胸交界处,呈现出主动脉扭结的表现。通过磁共振成像(RMI)以及主动脉造影进行了补充评估。胸部闪烁扫描显示左肺灌注不足。心脏评估的其余部分正常。患者在股-股体外循环下通过第4肋间间隙的左后外侧开胸手术进行治疗。检查发现降胸主动脉有一个直径7厘米的钙化动脉瘤,合并与延长和扭结相关的严重狭窄。主动脉上段向胸膜顶移位。动脉瘤上方的主动脉段大小正常,而下方段扩张。切除动脉瘤并进行了人工血管移植。手术随访期间血流动力学稳定,无神经功能缺损。术后需要5天的通气辅助。目前随访8个月,患者情况良好。
鉴于假性缩窄(动脉高血压、主动脉瓣关闭不全)或动脉瘤本身(夹层、对周围组织如肺动脉的压迫)继发并发症的风险,对于这种类型的动脉瘤进行人工血管置换是合理的。