Smythe W R, Bridges N D, Gaynor J W, Nicolson S, Clark B J, Spray T L
Department of Anesthesiology, The Children's Hospital of Philadelphia, Pennsylvania 19104, USA.
Ann Thorac Surg. 2000 Aug;70(2):654-6. doi: 10.1016/s0003-4975(00)01571-x.
A case of bilateral sequential lung transplantation for anhidrotic ectodermal dysplasia is presented. The patient was a 16-year-old male with end-stage lung disease secondary to chronic severe respiratory infection. Although a relatively rare disease, the common association of fatal pulmonary compromise in those affected with this disorder warrants consideration of lung transplantation as a viable therapeutic option.
本文介绍了一例因无汗性外胚层发育不良而行双侧序贯肺移植的病例。患者为一名16岁男性，患有慢性严重呼吸道感染继发的终末期肺病。尽管这种疾病相对罕见，但患有该疾病的患者常伴有致命的肺部损害，这使得肺移植成为一种可行的治疗选择。
