Nardone R, Bernhart H, Pozzera A, Taddei M, Tezzon F
Division of Neurology, F. Tappeiner Hospital, Merano, Italy.
Neurol Sci. 2000 Jun;21(3):177-81. doi: 10.1007/s100720070094.
An isolated affection of the phrenic nerve is a rare feature in patients with neuralgic amyotrophy. We report 1 case each of bilateral and unilateral phrenic neuropathy. The first patient presented a sudden onset of severe respiratory failure without pain. The second patient developed intense pain in the neck and in the right shoulder followed by dyspnea on mild effort and orthopnea. Chest X-rays showed elevation of the diaphragm. Needle electromyography revealed denervation restricted to the diaphragm. The phrenic nerve conduction was within the normal range. The diagnosis of neuralgic amyotrophy may be particularly difficult when the palsy of the phrenic nerve appears without brachial plexus involvement or the typical shoulder pain of acute onset. In our patients, electrophysiological evaluation combined with radiographic studies, ventilatory parameters and biochemical analyses were helpful in establishing the diagnosis.
在神经性肌萎缩患者中,膈神经孤立性受累是一种罕见的表现。我们报告了双侧和单侧膈神经病变各1例。首例患者突然出现严重呼吸衰竭且无疼痛。第二例患者先是颈部和右肩部剧痛,随后轻微用力时即出现呼吸困难及端坐呼吸。胸部X线片显示膈肌抬高。针极肌电图显示失神经改变仅限于膈肌。膈神经传导在正常范围内。当膈神经麻痹出现而无臂丛神经受累或无急性起病的典型肩部疼痛时,神经性肌萎缩的诊断可能特别困难。在我们的患者中,电生理评估结合影像学检查、通气参数及生化分析有助于明确诊断。