Kaku R, Oda T, Fujii Y, Esato K, Yamaki R
J Cardiovasc Surg (Torino). 1975 Jan-Feb;16(1):95-9.
A 14-year-old boy with an incomplete form of the Marfan syndrome developed an acute episode of severe congestive heart failure following exertion. The preoperative studies indicated a mitral insufficiency, and a floppy, thickened mitral valve was removed and replaced with a Starr-Edwards prosthesis. Microscopically, the valve showed increase in collagen with central myxomatous transformation. Seven months postoperatively the patient is doing well and has no symptoms of heart failure.
一名患有不完全型马凡综合征的14岁男孩在运动后出现了严重充血性心力衰竭的急性发作。术前检查显示二尖瓣关闭不全，遂将一个松弛、增厚的二尖瓣切除，并用斯塔尔-爱德华兹人工瓣膜进行置换。显微镜检查显示，瓣膜胶原增加并伴有中央黏液瘤样变性。术后七个月，患者情况良好，无心力衰竭症状。
