Biagini R, Tignani R, Fifi A R, Nappini L
Arch Dis Child. 1979 Aug;54(8):644-5. doi: 10.1136/adc.54.8.644.
A 14-year-old boy had suffered from intermittent acute hepatic porphyria, myoclonic convulsions and mental retardation (Lennox-Gastaut syndrome). The porphyria was treated by stopping the administration of phenobarbitone and phenytoin. Sodium valproate at a dose of 70 mg/kg per day lessened the severity and frequency of convulsive crises.
一名14岁男孩患有间歇性急性肝卟啉症、肌阵挛性惊厥和智力发育迟缓（伦诺克斯-加斯托综合征）。通过停用苯巴比妥和苯妥英钠来治疗卟啉症。每天70毫克/千克剂量的丙戊酸钠减轻了惊厥发作的严重程度和频率。
