Dardas P S, Tsikaderis D D, Mezilis N, Geleris P, Boudoulas H
Thessaloniki Heart Institute, St Lukas Hospital, Thessaloniki, Greece.
Eur J Echocardiogr. 2002 Dec;3(4):303-5.
Cardiac involvement occurs in up to 50% of patients with primary amyloidosis. Diffuse amyloid deposits lead to impairment of myocardial systolic and diastolic function. Due to the severe left ventricular diastolic abnormality, left atrial contribution to left ventricular stroke volume remains critical. We report a case of primary amyloidosis where we assessed non-invasively left atrial systolic function.
原发性淀粉样变性患者中,高达50%会出现心脏受累。弥漫性淀粉样蛋白沉积会导致心肌收缩和舒张功能受损。由于严重的左心室舒张功能异常,左心房对左心室每搏输出量的贡献仍然至关重要。我们报告一例原发性淀粉样变性病例,在此病例中我们对左心房收缩功能进行了无创评估。