Ferrándiz C, Lecha M, Aguadé J P
Med Cutan Ibero Lat Am. 1975;3(5):353-9.
An observation of Scleromyxedema is repported by the authors. The remarkable peculiarities of this case are the following: 1. Absence of abnormal paraprotein. 2. Positive direct and indirect immunofluorescence. 3. Slight increase of plasma cells of bone marrow. 4. Presence of calcifications. 5. The hyperkeratotic lesions. Those of the fingertips with histology of porokeratosis. 6. Scarcity of the metachromatic depots of muchopolisacharids in the dermis evident only with the Alcian-PAS stain.
作者报告了1例硬化性黏液水肿。该病例的显著特点如下：1. 无异常副蛋白。2. 直接和间接免疫荧光阳性。3. 骨髓浆细胞轻度增多。4. 存在钙化。5. 角化过度性损害，指尖处组织学表现为汗孔角化病。6. 真皮中酸性黏多糖异染性沉积物稀少，仅阿尔辛-过碘酸雪夫染色时明显。
