Malignant renal epithelioid angiomyolipoma with aggressive behavior and distant metastasis.

Angiomyolipoma (AML) is a common renal tumor and mostly benign in entity. Malignant AML is extremely rare and most of them are found to be epithelioid AML histopathologically. We report the imaging features of a malignant epithelioid AML in a 58-year-old patient with liver and nodal metastases, and review the literatures. We have observed that AML of epithelioid subtype with tumoral necrosis may suggest the malignant change.