Leclerc J C, Marchal F, Stines J, Régent D
Service de Radiologie, hôpital d'adultes, CHU Nancy Brabois, 54500 Vandoeuvre les Nancy.
J Radiol. 2003 Jul-Aug;84(7-8 Pt 1):851-4.
Angiomyolipoma is a well-known rare soft tissue tumor involving the kidneys, liver and other organs. Long believed to be a benign hamartoma, angiomyolipoma is now considered a neoplasm that arises from perivascular epithelioid cell. Epithelioid angiomyolipoma is a rare variant of angiomyolipoma characterized by epithelioid cells that mimic renal cell carcinoma and is potentially malignant. Immunoreactivity with HMB45 is helpful for its identification. We report the computed tomographic and histologic findings in a 36 years old woman with epithelioid angiomyolipoma and lymph node involvement.
血管平滑肌脂肪瘤是一种累及肾脏、肝脏和其他器官的罕见软组织肿瘤。长期以来，血管平滑肌脂肪瘤一直被认为是一种良性错构瘤，现在被认为是一种起源于血管周上皮样细胞的肿瘤。上皮样血管平滑肌脂肪瘤是血管平滑肌脂肪瘤的一种罕见变体，其特征是上皮样细胞类似肾细胞癌，具有潜在恶性。HMB45免疫反应性有助于其识别。我们报告了一名36岁患有上皮样血管平滑肌脂肪瘤并伴有淋巴结受累的女性的计算机断层扫描和组织学检查结果。
