Rouveyrol F, Stephan J L
Servide de pédiatrie, Hôtel-Dieu, 63000 Clermont-Ferrand, France.
Arch Pediatr. 2003 Jun;10(6):527-9. doi: 10.1016/s0929-693x(03)00168-4.
Benign paroxysmal tonic upgaze is an ill-defined neuro-ophthalmological disorder with onset in infancy. It consists of sudden ocular movements with sustained upward deviation of the eyes. Episodes disappear with time: spontaneous remission occurs within a few months or years without any change in psychomotor development. EEG and neuro-imaging are unrevealing. To date, the pathogenesis of the condition is still unknown. Early recognition of this benign condition minimizes potentially unnecessary investigations and treatments. Herein, we report on 2 additional sporadic cases.
良性阵发性强直性上视是一种定义不明确的神经眼科疾病，起病于婴儿期。它表现为突发的眼球运动，伴有双眼持续向上偏斜。发作会随时间消失：在几个月或几年内会自发缓解，且精神运动发育无任何变化。脑电图和神经影像学检查无异常发现。迄今为止，该疾病的发病机制仍不清楚。早期识别这种良性疾病可减少潜在的不必要检查和治疗。在此，我们报告另外2例散发性病例。
