特发性阵发性强直向上凝视。

Idiopathic paroxysmal tonic upward gaze.

机构信息

Department of Neurology, School of Medicine, Ege University, Izmir, Turkey.

出版信息

Pediatr Neurol. 2012 Oct;47(4):306-8. doi: 10.1016/j.pediatrneurol.2012.05.028.

DOI:10.1016/j.pediatrneurol.2012.05.028

Abstract

Paroxysmal tonic upward gaze constitutes a neuro-ophthalmologic syndrome characterized by episodes of sustained conjugate upward deviation of the eyes, normal horizontal gaze, and ataxia. Its pathogenesis is unknown, and the etiology is heterogeneous. The prognosis is variable. We present a case of "idiopathic paroxysmal tonic upward gaze" with a positive clinical course and spontaneous remission.

摘要

阵发性强直性向上凝视构成一种神经眼科综合征，其特征为眼部持续向上共轭性偏斜、水平凝视正常和共济失调。其发病机制不明，病因呈异质性。预后不定。我们报告了一例“特发性阵发性强直性向上凝视”病例，其临床表现呈阳性且自发缓解。