St Cyr J A, Campbell D N, Fullerton D A, Grosso M, Bishop D A, Clarke D R
Cardiothoracic Surgery, University of Colorado Health Sciences Center, Children's Hospital, Denver 80218.
Ann Thorac Surg. 1992 Jun;53(6):1110-3. doi: 10.1016/0003-4975(92)90402-p.
Mortality for interruption of the aortic arch approaches 100% within the first year of life if untreated. Prostaglandin E1 can stabilize the patient's condition in anticipation of surgical palliation, but total repair is required for long-term survival. Successful complete repair of type B interrupted aortic arch, hypoplasia of the left ventricular outflow tract, and ventricular septal defect was possible using a cryopreserved allograft in a child who previously had undergone unusual palliation.
如果不进行治疗，主动脉弓中断的患儿在出生后第一年内死亡率接近100%。前列腺素E1可在预期进行手术姑息治疗前稳定患者病情，但要实现长期存活则需要进行完全修复。一名此前接受过特殊姑息治疗的儿童，使用冷冻保存的同种异体移植物成功完成了B型主动脉弓中断、左心室流出道发育不全和室间隔缺损的完全修复。
