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先天性横纹肌肉瘤1例罕见病例(作者译)

[A rare case of congenital rhabdomyosarcoma (author's transl)].

作者信息

Foet K, Prott W

出版信息

Laryngol Rhinol Otol (Stuttg). 1977 Jun;56(6):528-32.

PMID:141570
Abstract

A case of a two-weeks-old female infant is reported who was born with an embryonal rhabdomyosarcoma in the size of more than a man's fist that was located in the area of the left half of the face. The tumor provoked an extreme disfiguration by its rapid postpartial growth when metastases had already developed. A palliative operation in order to maintain respiration and nutrition was performed when exitus letalis occured in hemorrhagical shock and consecutive circulatory break-down.

摘要

报告了一例两周大的女婴,她出生时患有胚胎性横纹肌肉瘤,肿瘤大小超过一个人的拳头,位于左半脸区域。肿瘤术后迅速生长并发生转移,导致严重毁容。当患儿因失血性休克和随后的循环衰竭死亡时,进行了姑息性手术以维持呼吸和营养。

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