Canarelli J P, Pautard B, Ricard J, Bobyono J M, Collet L M, Risbourg B
Service de Chirurgie Pédiatrique, CHU, Amiens.
Chir Pediatr. 1988;29(6):349-51.
A case report of congenital embryonal rhabdomyosarcoma of the superior extremity (right shoulder) is described. This patient was the first and only child of a 24 year-old woman who had been previously treated for sterility. The diagnosis was done by echography during the 36 th week of gestation. This full term white boy was born by cesarean section in reason of tumor size. First he was treated surgically. Then, a cyclic chemotherapy (VAC) was performed. After 4 courses, local recurrence led to a second surgical excision followed by a new cyclic chemotherapy (IVA). The treatment had an acceptable tolerance. Seven months later the child is free disease alive.
本文描述了一例上肢(右肩)先天性胚胎性横纹肌肉瘤的病例报告。该患者是一名24岁曾接受过不育治疗的女性的首个也是唯一的孩子。在妊娠第36周时通过超声检查做出诊断。由于肿瘤大小,这名足月白人男孩通过剖宫产出生。首先对他进行了手术治疗。然后,进行了周期性化疗(VAC方案)。4个疗程后,局部复发导致进行了第二次手术切除,随后进行了新的周期性化疗(IVA方案)。治疗耐受性尚可。七个月后,患儿无病存活。