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Congenital dysplasia of the interlobular bile ducts with extensive skin xanthomata; congenital acholangic biliary cirrhosis.

作者信息

MacMAHON H E, THANNHAUSER S J

出版信息

Gastroenterology. 1952 Aug;21(4):488-506.

PMID:14955017
Abstract
摘要

相似文献

1
Congenital dysplasia of the interlobular bile ducts with extensive skin xanthomata; congenital acholangic biliary cirrhosis.先天性小叶间胆管发育异常伴广泛皮肤黄瘤；先天性无胆管性胆汁性肝硬化。
Gastroenterology. 1952 Aug;21(4):488-506.
2
Destructive intrahepatic bile duct diseases.肝内胆管破坏性疾病
Recenti Prog Med. 1990 Jun;81(6):392-8.
3
Absence of interlobular bile ducts. Report of a case of probable intrahepatic bile duct agenesis with severe hypercholesterolemia, xanthomatosis, and glomerular lipid deposition.小叶间胆管缺如。一例可能为肝内胆管发育不全伴严重高胆固醇血症、黄瘤病和肾小球脂质沉积的病例报告。
Am J Dis Child. 1961 Feb;101:228-37.
4
[CONGENITAL CYSTIC BILIARY FIBRO-ADENOMATOSIS].[先天性囊性胆管纤维腺瘤病]
Rev Int Hepatol. 1964;14:467-88.
5
[Bile duct atresia, bile duct hypoplasia].[胆管闭锁，胆管发育不全]
Hippokrates. 1974 May;45(2):242-5.
6
Surgical treatment of congenital dilatation of the biliary system.先天性胆管系统扩张症的外科治疗
Ital J Surg Sci. 1985;15(2):189-97.
7
[Agenesis of the intrahepatic bile ducts with normal extrahepatic biliary tract. Anatomical study].[肝内胆管缺如伴肝外胆道正常。解剖学研究]
Arch Fr Pediatr. 1961 Mar;18:358-67.
8
Expression of beta 2-microglobulin on interlobular bile ducts in primary biliary cirrhosis and other hepatobiliary diseases.原发性胆汁性肝硬化及其他肝胆疾病小叶间胆管中β2微球蛋白的表达
Acta Pathol Jpn. 1988 Jul;38(7):853-60. doi: 10.1111/j.1440-1827.1988.tb02357.x.
9
[Congenital agenesis of intrahepatic bile ducts].[先天性肝内胆管缺如]
Maandschr Kindergeneeskd. 1962 Feb;30:56-68.
10
[Agenesis of the intrahepatic bile ducts].[肝内胆管缺如]
Helv Paediatr Acta. 1953 Aug;8(4):281-94.

引用本文的文献

1
[Biliary xanthomatosis in adults and children; acquired pericholangitic biliary cirrhosis].[成人及儿童的胆汁性黄瘤病；获得性胆管周围性胆汁性肝硬化]
Virchows Arch Pathol Anat Physiol Klin Med. 1952;321(6):664-8. doi: 10.1007/BF00956306.
2
Histogenesis of hepatic cirrhosis studied by the threedimensional approach.采用三维方法研究肝硬化的组织发生。
Am J Pathol. 1955 May-Jun;31(3):405-41.
3
[ON THE EMBRYOLOGY AND CONGENITAL HYPERPLASIA OF THE INTRAHEPATIC BILE DUCTS WITH PERILOBULAR AND NODULAR LIVER FIBROSIS].[关于肝内胆管的胚胎学及先天性增生伴小叶周围和结节性肝纤维化]
Virchows Arch Pathol Anat Physiol Klin Med. 1965 Jan 15;338:210-23.
4
Paucity of interlobular bile ducts: getting to know it better.小叶间胆管稀少：进一步了解它
Dig Dis Sci. 1981 Jun;26(6):481-4. doi: 10.1007/BF01308095.
5
[Histological differential diagnosis of obstructive jaundice in early childhood].[幼儿期梗阻性黄疸的组织学鉴别诊断]
Langenbecks Arch Chir. 1972;332:677-96. doi: 10.1007/BF01282714.
6
Glomerular mesangiolipidosis in Alagille syndrome (arteriohepatic dysplasia).阿拉吉耶综合征（动脉肝发育不良）中的肾小球系膜脂质沉积症。
Pediatr Nephrol. 1987 Jul;1(3):455-64. doi: 10.1007/BF00849254.
7
[Hypertension and bilateral stenosis of the renal artery associated with congenital hypoplasia of the intrahepatic bile ducts (author's transl)].高血压与双侧肾动脉狭窄合并先天性肝内胆管发育不全（作者译）
Eur J Pediatr. 1976 Jan 2;121(2):125-39. doi: 10.1007/BF00443067.
8
The metabolism of 3alpha, 7alpha, 12alpha-trihydorxy-5beta-cholestan-26-oic acid in two siblings with cholestasis due to intrahepatic bile duct anomalies. An apparent inborn error of cholic acid synthesis.两名因肝内胆管异常导致胆汁淤积的同胞中3α, 7α, 12α-三羟基-5β-胆甾烷-26-酸的代谢。一种明显的胆酸合成先天性缺陷。
J Clin Invest. 1975 Sep;56(3):577-87. doi: 10.1172/JCI108127.