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发生于巨大先天性黑素细胞痣的横纹肌肉瘤。

Rhabdomyosarcoma arising in a giant congenital melanocytic nevus.

作者信息

Ilyas Erum N, Goldsmith Kelly, Lintner Rebecca, Manders Steven M

机构信息

Department of Medicine, Division of Dermatology, Cooper Health System, Robert Wood Johnson, University of Medicine and Dentistry of New Jersey at Camden, 100 Brick Rd, Suite 306, Marlton, NJ 08053, USA.

出版信息

Cutis. 2004 Jan;73(1):39-43.

PMID:14964630
Abstract

We report the case of a 6-week-old girl who presented with a pedunculated embryonal rhabdomyosarcoma arising in a giant congenital melanocytic nevus (GCMN) on her lower back. There was no associated leptomeningeal involvement. The patient underwent surgical resection of the rhabdomyosarcoma at age 2 months, with subsequent chemotherapy consisting of actinomycin D and vincristine. No recurrences or metastases of tumor have been noted at 5 months of age.

摘要

我们报告了一名6周大女童的病例,她下背部的巨大先天性黑素细胞痣(GCMN)出现了带蒂的胚胎性横纹肌肉瘤。未发现软脑膜受累。该患者在2个月大时接受了横纹肌肉瘤的手术切除,随后接受了由放线菌素D和长春新碱组成的化疗。在5个月大时未发现肿瘤复发或转移。

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Rhabdomyosarcoma arising in a congenital melanocytic nevus.先天性黑素细胞痣中发生的横纹肌肉瘤。
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引用本文的文献

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Congenital melanocytic neoplasms: clinical, histopathological and recent molecular developments.先天性黑素细胞肿瘤:临床、组织病理学及近期分子进展
Virchows Arch. 2025 Jan;486(1):165-176. doi: 10.1007/s00428-024-04011-3. Epub 2025 Jan 15.
2
Rhabdomyosarcoma Arising in a Giant Congenital Melanocytic Naevus: Case Report and Literature Review.发生于巨大先天性黑素细胞痣的横纹肌肉瘤:病例报告及文献复习
Dermatopathology (Basel). 2019 Jun 26;6(2):91-98. doi: 10.1159/000496337. eCollection 2019 Apr-Jun.