Taylor I, Parsons Mark
Department of Neurology, Royal Melbourne Hospital, Parkville, Vic. 3050, Australia.
J Clin Neurosci. 2004 Apr;11(3):319-21. doi: 10.1016/j.jocn.2003.04.004.
A rare case of a lady with acute hypokalemic quadriparesis and underlying distal renal tubular acidosis manifesting as a presentation of Sjögren's syndrome is described. The case highlights the concept that acute hypokalemia due to unrecognized renal tubular acidosis may unmask Sjögren's syndrome in patients without sicca symptoms and it may be a marker of more severe renal disease. Acute paralysis is a life threatening consequence of hypokalemia and when due to potassium wasting secondary to renal tubular acidosis may be easily prevented. Underlying Sjögren's syndrome should be considered in all patients of either sex and at any age presenting with hypokalemic paralysis.
本文描述了一例罕见病例,一名女性患有急性低钾性四肢瘫,其潜在的远端肾小管酸中毒表现为干燥综合征。该病例凸显了这样一个概念,即未被识别的肾小管酸中毒所致的急性低钾血症可能会在无干燥症状的患者中揭示干燥综合征,且这可能是更严重肾脏疾病的一个标志。急性麻痹是低钾血症危及生命的后果,而由肾小管酸中毒继发的钾耗竭所致的急性麻痹很容易预防。对于所有出现低钾性麻痹的患者,无论性别和年龄,均应考虑其潜在的干燥综合征。