Maisawa S, Takasago Y, Oyake Y, Maeta H, Fujiwara T
Department of Paediatrics, Morioka Children's Hospital, Japan.
Eur J Pediatr. 1992 Aug;151(8):569-71. doi: 10.1007/BF01957722.
We report a functioning ductus venosus with hypoplasia of the right hepatoportal system in a 2-year-old child born with asymmetric intra-uterine growth retardation. Postprandial galactosaemia and hyperammonaemia were clues to diagnosis of portal-systemic shunt through the patent ductus venosus, which was confirmed by ultrasonography and angiography.
我们报告了一名2岁儿童,其患有右肝门静脉系统发育不全,但静脉导管功能正常,该儿童出生时患有不对称性宫内生长迟缓。餐后半乳糖血症和高氨血症是通过开放的静脉导管发生门体分流诊断的线索,这一点通过超声检查和血管造影得以证实。