Yalçinbaş Yusuf Kenan, Erek Ersin, Salihoğlu Ece, Oztürk Nilüfer, Mamur Gökhan, Soybir Nerime, Sarioğlu Ayşe, Sarioğlu Tayyar
Istanbul Memorial Hospital, Istanbul, Turkey.
Turk J Pediatr. 2004 Apr-Jun;46(2):179-81.
Total anomalous pulmonary venous return (TAPVR) is a rare congenital pathology. Early diagnosis and urgent surgery are life-saving, especially in newborns with pulmonary venous obstruction, which is most commonly seen with infracardiac type. A three-day-old baby boy presented to another clinic with tachypnea and cyanosis. Initial work-up aimed at ruling out persistant pulmonary hypertension, respiratory distress syndrome and pneumonia. Acute pulmonary edema then developed, and on echocardiography obstructive type infracardiac TAPVR was suspected. Cardiac catheterization was done for definitive diagnosis. Urgent surgery was undertaken and pulmonary veins were anastomozed to left atrium with posterior approach. Patient was extubated at 10th day and discharged after three weeks. During one-year follow-up the patient was free of symptoms. Infracardiac type TAPVR is a rare pathology in which early diagnosis and urgent surgery with special postoperative case are mandatory for survival.
完全性肺静脉异位引流(TAPVR)是一种罕见的先天性疾病。早期诊断和紧急手术是挽救生命的关键,特别是对于伴有肺静脉梗阻的新生儿,这种情况在心脏下型最为常见。一名3天大的男婴因呼吸急促和发绀被送往另一家诊所。初步检查旨在排除持续性肺动脉高压、呼吸窘迫综合征和肺炎。随后出现急性肺水肿,经超声心动图检查怀疑为梗阻型心脏下型TAPVR。为明确诊断进行了心导管检查。进行了紧急手术,采用后入路将肺静脉与左心房吻合。患者在第10天拔管,三周后出院。在一年的随访中,患者无症状。心脏下型TAPVR是一种罕见的疾病,早期诊断和采用特殊术后护理的紧急手术是生存的必要条件。