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原发性心脏横纹肌肉瘤的完整切除

COMPLETE RESECTION OF A PRIMARY CARDIAC RHABDOMYOSARCOMA.

作者信息

Schwartz Judy E., Schwartz Gary P., Judson Preston L., Seibel John E., Trumbull Horace R.

机构信息

Department of Surgery, Uniformed Services University of the Health Sciences.

出版信息

Cardiovasc Dis. 1979 Dec;6(4):413-424.

PMID:15216294
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC287816/
Abstract

A case of primary cardiac rhabdomyosarcoma in a 23-year-old white man was managed by complete excision and combination chemotherapy. The pathologic features of the tumor are described. Based on a review of the English literature, the natural history of this tumor is discussed and a plan of therapy is proposed, which consists of (1) resection of the tumor if feasible, (2) chemotherapy with Actinomycin D, vincristine sulfate, and cyclophosphamide, and (3) cardiac radiation for residual unresected or locally recurrent tumor.

摘要

一名23岁白人男性原发性心脏横纹肌肉瘤患者接受了肿瘤完全切除及联合化疗。文中描述了该肿瘤的病理特征。在回顾英文文献的基础上,讨论了该肿瘤的自然病史,并提出了一种治疗方案,包括:(1)可行时切除肿瘤;(2)使用放线菌素D、硫酸长春新碱和环磷酰胺进行化疗;(3)对残留未切除或局部复发肿瘤进行心脏放疗。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/60d9/287816/5b2703a7b8b2/cardiodis00012-0045-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/60d9/287816/415527beac2d/cardiodis00012-0044-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/60d9/287816/9be3d33adbb6/cardiodis00012-0045-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/60d9/287816/5b2703a7b8b2/cardiodis00012-0045-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/60d9/287816/415527beac2d/cardiodis00012-0044-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/60d9/287816/9be3d33adbb6/cardiodis00012-0045-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/60d9/287816/5b2703a7b8b2/cardiodis00012-0045-b.jpg

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引用本文的文献

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Left atrial rhabdomyosarcoma and the use of digital gated computed tomography in its diagnosis.左心房横纹肌肉瘤及数字门控计算机断层扫描在其诊断中的应用。
Br Heart J. 1986 Mar;55(3):305-7. doi: 10.1136/hrt.55.3.305.

本文引用的文献

1
Primary rhabdomyosarcoma of the heart and complete atrioventricular block. A case report and review of the literature.
Am J Med. 1961 Nov;31:820-27. doi: 10.1016/0002-9343(61)90167-x.
2
Primary rhabdomyosarcoma of the heart with metastases.原发性心脏横纹肌肉瘤伴转移
AMA Arch Pathol. 1955 Jun;59(6):669-72.
3
Primary malignant tumor of the heart in infancy; case report and review of the subject.婴儿期原发性心脏恶性肿瘤;病例报告及相关主题综述
Pediatrics. 1955 May;15(5):562-74.
4
SUCCESSFUL STERILIZATION OF A PRIMARY CARDIAC SARCOMA BY SUPERVOLTAGE RADIATION THERAPY.超高压放射治疗成功治愈原发性心脏肉瘤
Am J Roentgenol Radium Ther Nucl Med. 1964 Oct;92:942-6.
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PRIMARY SARCOMA OF THE MITRAL VALVE.二尖瓣原发性肉瘤
Am Heart J. 1963 Aug;66:243-7. doi: 10.1016/0002-8703(63)90040-1.
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Rhabdomyosarcoma of the left atrium.左心房横纹肌肉瘤
Br Heart J. 1960 Sep;22(4):597-600. doi: 10.1136/hrt.22.4.597.
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Anaplastic myxoma of left atrium.左心房间变性黏液瘤
AMA Arch Intern Med. 1957 Nov;100(5):819-26. doi: 10.1001/archinte.1957.00260110135019.
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Intracavitary cardiac neoplasms. A review of fifteen cases.心腔内肿瘤。15例病例回顾。
Br Heart J. 1966 Jan;28(1):75-83. doi: 10.1136/hrt.28.1.75.
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Treatment of primary angiosarcoma of the heart.心脏原发性血管肉瘤的治疗
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Southwest Med. 1969 Aug;50(8):128-33.