Kubota Yuichi, Kawamata Takakazu, Kubo Osami, Kasuya Hidetoshi, Muragaki Yoshihiro, Hori Tomokatsu
Department of Neurosurgery, Neurological Institute, Tokyo Women's Medical University, 8-1 Kawada-Cho, Tokyo, 162-8666, Japan.
Neurosurg Rev. 2005 Jul;28(3):234-8. doi: 10.1007/s10143-005-0381-x. Epub 2005 Mar 8.
Although approximately 30% of facial nerve schwannoma cases present with no facial palsy, a large facial nerve schwannoma extending to the middle and posterior cranial fossa quite rarely presents without facial palsy. The authors encountered two patients with large facial nerve schwannoma who presented with only hearing impairment and no facial palsy. The first patient was a 64-year-old woman who presented with right auditory impairment without facial palsy. MR images demonstrated a dumbbell-shaped tumor in the cerebellopontine angle. Another patient, a 40-year-old woman, also presented with vertigo and right tinnitus without facial palsy. MR images demonstrated a huge tumor expanding into both the posterior cranial fossa and middle cranial fossa. In both cases, intraoperative findings confirmed that the tumors had grown from the facial nerve. Facial nerve schwannoma can be easily diagnosed if detailed neurological evaluations and appropriate neuroimagings are conducted. However, in spite of such huge tumoral size and expanding pattern, the facial nerve function was relatively preserved. Anatomical features of the facial schwannoma are discussed. A tumor extending to the middle and posterior cranial fossa should remind neurosurgeons to consider facial nerve schwannomas even in the absence of facial palsy.
尽管约30%的面神经鞘瘤病例无面神经麻痹表现,但累及中颅窝和后颅窝的大型面神经鞘瘤极少有无面神经麻痹的情况。作者遇到两例大型面神经鞘瘤患者,他们仅表现为听力障碍而无面神经麻痹。第一例患者是一名64岁女性,表现为右侧听觉障碍且无面神经麻痹。磁共振成像(MR)显示桥小脑角有哑铃形肿瘤。另一例患者是一名40岁女性,也表现为眩晕和右侧耳鸣且无面神经麻痹。MR图像显示一个巨大肿瘤扩展至后颅窝和中颅窝。在这两例中,术中发现均证实肿瘤起源于面神经。如果进行详细的神经学评估和适当的神经影像学检查,面神经鞘瘤很容易诊断。然而,尽管肿瘤体积巨大且呈扩展模式,但面神经功能相对得以保留。本文讨论了面神经鞘瘤的解剖学特征。即使在无面神经麻痹的情况下,延伸至中颅窝和后颅窝的肿瘤也应提醒神经外科医生考虑面神经鞘瘤。