McKinney Craig A, Geiger James D, Castle Valerie P, Ruiz Robert E, Strouse Peter J
Department of Pediatric Surgery, CS Mott Children's Hospital, University of Michigan Health System, Ann Arbor, Michigan, USA.
Pediatr Hematol Oncol. 2005 Jan-Feb;22(1):17-24. doi: 10.1080/08880010590896206.
Angiomyolipoma is a tumor of the kidney and, more rarely, the liver, which histologically consists of smooth muscle cells, adipose cells, and abnormal blood vessels in varying proportions. This tumor is generally benign and resection is curative, but here the authors present the case of a 14-year-old girl with an unusual primary hepatic angiomyolipoma that recurred following resection and behaved aggressively. Despite stabilization with a number of novel therapies, the child ultimately died of progressive disease.
